The Mount Sinai Hospital Clinicopathological conference: A 45-year-old man with Pompe's disease and dilated cardiomyopathy

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Abstract

This is an unusual case of a 45-year-old man, born in Ecuador, with evidence of profound left ventricular dysfunction, dilated cardiomyopathy and marked myocardial hypertrophy. Preceding events were advanced atrioventricular block (necessitating pacemaker implantation) and atrial flutter. The diagnosis of Pompe's disease was established by endomyocardial biopsy and appropriate staining, which indicated abnormal glycogen storage.

Original languageEnglish
Pages (from-to)205-212
Number of pages8
JournalMount Sinai Journal of Medicine
Volume68
Issue number3
StatePublished - May 2001

Keywords

  • Chagas' disease
  • Congestive heart failure
  • Dilated cardiomyopathy
  • Fabry's disease
  • Glycogen storage disease
  • Heart block
  • Pompe's disease
  • Ventricular dysfunction

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