Steroid-responsive encephalopathy associated with autoimmune thyroiditis (SREAT) presenting with pure cerebellar ataxia

Pichet Termsarasab, Yuvadee Pitakpatapee, Steven J. Frucht, Prachaya Srivanitchapoom

Research output: Contribution to journalArticlepeer-review

6 Scopus citations

Abstract

Background: Myoclonus and tremor are common movement disorder phenomenologies in steroid-responsive encephalopathy associated with autoimmune thyroiditis (SREAT). Pure ataxia without encephalopathy has rarely been reported. Case report: We report 21- and 40-year-old females who presented with subacute pure ataxia without encephalopathy. After immunotherapies, both exhibited initial improvement of ataxia, and subsequently remained in plateau phase. Discussion: This treatable disorder should be added to the differential diagnoses of progressive cerebellar ataxia, and anti-thyroid peroxidase and antithyroglobulin should be considered as part of the workup. It is crucial not to misdiagnose SREAT presenting with pure cerebellar ataxia as degenerative or spinocerebellar ataxia.

Original languageEnglish
JournalTremor and Other Hyperkinetic Movements
Volume8
DOIs
StatePublished - 2018
Externally publishedYes

Keywords

  • Ataxia
  • Autoimmune
  • Autoimmune thyroiditis
  • Hashimoto encephalopathy
  • Movement disorders
  • SREAT
  • Steroid-responsive encephalopathy associated with autoimmune thyroiditis

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