Redirection of hepatic drainage for treatment of pulmonary arteriovenous malformations following the Fontan procedure

I. Hui Wu, Khanh H. Nguyen

Research output: Contribution to journalArticlepeer-review

20 Scopus citations

Abstract

The development of unilateral pulmonary arteriovenous malformations in patients after total cavopulmonary connection with an extracardiac conduit has been reported. Unequal distribution of hepatic venous flow to the lung is theorized to be the causative factor. We report the surgical management of pulmonary arteriovenous malformations in a patient with heterotaxy syndrome, single ventricle, and interrupted inferior vena cava. The patient had previously undergone a total cavopulmonary connection with an extracardiac conduit draining hepatic venous flow to the right branch pulmonary artery. In the subsequent operation, we redirected the extracardiac conduit to the innominate vein. This operation provided the affected lung with hepatic venous blood without exposing the patient to the morbidity associated with cardiopulmonary bypass.

Original languageEnglish
Pages (from-to)519-522
Number of pages4
JournalPediatric Cardiology
Volume27
Issue number4
DOIs
StatePublished - Aug 2006

Keywords

  • Cardiopulmonary bypass
  • Fontan procedure
  • Pulmonary arteriovenous malformations

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