TY - JOUR
T1 - Omovertebral bone causing traumatic compression of the cervical spinal cord and acute neurological deficits in a patient with Sprengel’s deformity and Klippel-Feil syndrome
T2 - Case report
AU - Pompliano, Michael
AU - Changoor, Stuart
AU - Mease, Samuel
AU - Emami, Cyrus
AU - Sinha, Kumar
AU - Hwang, Ki Soo
N1 - Publisher Copyright:
© AANS 2021, except where prohibited by US copyright law
PY - 2021/1
Y1 - 2021/1
N2 - The presence of an omovertebral bone with Sprengel’s deformity and Klippel-Feil syndrome is a complex congenital anomaly that is not well understood. It most commonly manifests as cosmetic deformity, limited range of motion, and functional disability, although there are reports of the insidious development of cervical myelopathy. In this paper, the authors present the case of a 49-year-old man with acute neurological deficits after a low-energy mechanism of traumatic spinal cord compression, resulting from an impinging omovertebral bone through a traumatic laminar defect. The patient underwent resection of the omovertebral bone, laminectomy decompression of the spinal canal, and anterior stabilization. This case highlights a rarely discussed complication of undiagnosed Sprengel’s deformity and its associated conditions following even low-energy traumatic mechanisms.
AB - The presence of an omovertebral bone with Sprengel’s deformity and Klippel-Feil syndrome is a complex congenital anomaly that is not well understood. It most commonly manifests as cosmetic deformity, limited range of motion, and functional disability, although there are reports of the insidious development of cervical myelopathy. In this paper, the authors present the case of a 49-year-old man with acute neurological deficits after a low-energy mechanism of traumatic spinal cord compression, resulting from an impinging omovertebral bone through a traumatic laminar defect. The patient underwent resection of the omovertebral bone, laminectomy decompression of the spinal canal, and anterior stabilization. This case highlights a rarely discussed complication of undiagnosed Sprengel’s deformity and its associated conditions following even low-energy traumatic mechanisms.
KW - Acute neurological deficits
KW - Congenital
KW - Klippel-Feil syndrome
KW - Omovertebral bone
KW - Sprengel’s deformity
KW - Traumatic spinal cord compression
UR - http://www.scopus.com/inward/record.url?scp=85098871152&partnerID=8YFLogxK
U2 - 10.3171/2020.6.SPINE20304
DO - 10.3171/2020.6.SPINE20304
M3 - Article
C2 - 32977313
AN - SCOPUS:85098871152
SN - 1547-5654
VL - 34
SP - 32
EP - 36
JO - Journal of Neurosurgery: Spine
JF - Journal of Neurosurgery: Spine
IS - 1
ER -