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Neurocutaneous melanocytosis-associated malignant melanoma presenting with peritoneal seeding

  • Ugur Sener
  • , Kevin Elmore
  • , Keerthana Jayaseelan
  • , Joanne Porter
  • , Ashfaq Marghoob
  • , Marc K. Rosenblum
  • , Sofia Haque
  • , Yasmin Khakoo

Research output: Contribution to journalArticlepeer-review

7 Scopus citations

Abstract

Neurocutaneous melanocytosis (NCM) is characterized by melanocyte deposition in the leptomeninges and brain parenchyma, primarily occurring in children with large or giant congenital melanocytic nevi (LCMN) or multiple congenital melanocytic nevi. Patients with NCM may develop hydrocephalus and increased intracranial pressure, which can be managed with ventriculoperitoneal (VP) shunting. We present the case of a 16-month-old girl who developed peritoneal carcinomatosis and malignant ascites following VP shunting for hydrocephalus secondary to NCM to increase awareness of this rare, but serious, complication of cerebrospinal fluid diversion.

Original languageEnglish
Pages (from-to)1298-1301
Number of pages4
JournalPediatric Dermatology
Volume38
Issue number5
DOIs
StatePublished - 1 Sep 2021
Externally publishedYes

Keywords

  • meningeal carcinomatosis
  • neoplasms malignant
  • neurocutaneous disorders
  • nevi-melanocytic
  • peritoneal carcinomatosis

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