Management of a cadaveric orthotopic liver transplantation in a pediatric patient with complex congenital heart disease

Dennis E. Feierman, Francine S. Yudkowitz, Joanne Hojsak, Sukru Emre

Research output: Contribution to journalArticlepeer-review

10 Scopus citations

Abstract

Pediatric orthotopic liver transplantations (OLT) are commonly performed nowadays. Two primary reasons for OLT in children are complications from either extrahepatic biliary atresia (EHBA) or inborn errors of metabolism. However, congenital liver disease may be associated with significant other congenital abnormalities. We present a case of a successful OLT in a pediatric patient with a history of EHBA, situs inversus, and complex congenital heart disease. The cardiac anomalies include dextrocardia, absence of the atrial septum (single atrium), single atrioventricular valve (a-v canal), and an incomplete ventricular septum. Prior surgery include a Kasai procedure for EHBA, banding of the proximal main pulmonary artery, and Broviac catheter placement. We present the anesthesia concerns and management for this complicated case.

Original languageEnglish
Pages (from-to)669-675
Number of pages7
JournalPaediatric Anaesthesia
Volume16
Issue number6
DOIs
StatePublished - Jun 2006

Keywords

  • Congenital heart disease
  • Liver
  • Transplantation

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