Juvenile dermatomyositis with Sjögren's syndrome

M. V. Holmes, Y. Ioannou, C. Borysiewicz, Debajit Sen

Research output: Contribution to journalArticlepeer-review

7 Scopus citations

Abstract

Juvenile dermatomyositis (JDM) is a rare disease, and Sjögren's syndrome (SS) is unusual in adolescents. We report the first case of biopsy-proven JDM and SS with pulmonary involvement. A 15-year-old adolescent boy presented with recurrent parotid gland hypertrophy, severe muscle weakness, pronounced skin rash and widespread lymphadenopathy. JDM was diagnosed by clinical examination, elevated muscle enzymes, electromyography and muscle biopsy; SS was diagnosed by xerostomia, anti-Ro (SS-A) positivity and histopathological analysis of salivary gland tissue. This case illustrates a systematic approach which we feel is especially important in the younger patient with a more plastic immune system.

Original languageEnglish
Pages (from-to)3-5
Number of pages3
JournalClinical Rheumatology
Volume27
Issue numberSUPPL. 1
DOIs
StatePublished - Jun 2008
Externally publishedYes

Keywords

  • Interstitial lung disease
  • Juvenile dermatomyositis
  • Myocarditis
  • Myositis
  • Sjögren's syndrome

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