We report on two schoolboys suffering from hereditary sensory neuropathy type IV (HSAN IV). HSAN IV is also referred to in English-speaking countries as CIPA, which stands for congenital insensitivity to pain and anhidrosis. Thus, this term names the cardinal symptoms of this extremely rare disease. In our article, in addition to symptoms and diagnostic procedures we illustrate the clinical course in both our patients, focusing on complications requiring reconstructive surgery of the hands and feet.
|Translated title of the contribution
|Hereditary sensory neuropathy type IV. Two case reports
|Number of pages
|Monatsschrift fur Kinderheilkunde
|Published - Mar 2007
- HSAN Type IV
- Hand surgery