Endosomal accumulation of Toll-like receptor 4 causes constitutive secretion of cytokines and activation of signal transducers and activators of transcription in Niemann-Pick disease type C (NPC) fibroblasts: A potential basis for glial cell activation in the NPC brain

Michitaka Suzuki, Yuko Sugimoto, Yuki Ohsaki, Makoto Ueno, Shinsuke Kato, Yukisato Kitamura, Hiroshi Hosokawa, Joanna P. Davies, Yiannis A. Ioannou, Marie T. Vanier, Kousaku Ohno, Haruaki Ninomiya

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Biochemistry, Genetics and Molecular Biology

Immunology and Microbiology

Neuroscience