Creutzfeldt-Jakob disease presenting as refractory nonconvulsive status epilepticus

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Abstract

A 70-year-old woman was admitted to the intensive care unit with refractory nonconvulsive status epilepticus. Extensive evaluation including neuroimaging and cerebrospinal fluid examination was unrevealing. Brain biopsy revealed spongiosis, and prion disease was confirmed by immunostaining, providing the diagnosis of Creutzfeldt-Jakob disease.

Original languageEnglish
Pages (from-to)345-348
Number of pages4
JournalJournal of Intensive Care Medicine
Volume19
Issue number6
DOIs
StatePublished - 2004
Externally publishedYes

Keywords

  • Brain biopsy
  • Creutzfeldt-Jakob disease
  • Prion
  • Status epilepticus

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