Colonic obstruction in a child with von Recklinghausen's neurofibromatosis

Marshall M. Stone, Brighita Weinberg, A. Robert Beck, Edith Grishman, Melvin Gertner

Research output: Contribution to journalArticlepeer-review

15 Scopus citations

Abstract

A child is reported who developed partial colonicobstruction from an intussuscepting polypoid mass in the transverse colon. A 5 cm plexiform ganglioneurofibroma was found at laparotomy. Examination of the entire gastrointestinal tract revealed no other neurogenic tumors. Gastrointestinal involvement by neurofibromatosis in children is rare; however, children with von Recklinghausen's disease who complain of vague abdominal symptoms should be evaluated for gastrointestinal tumors.

Original languageEnglish
Pages (from-to)741-743
Number of pages3
JournalJournal of Pediatric Surgery
Volume21
Issue number8
DOIs
StatePublished - Aug 1986

Keywords

  • Neurofibromatosis
  • colonic obstruction
  • von Recklinghausen's disease

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