Adamtsl2 deletion results in bronchial fibrillin microfibril accumulation and bronchial epithelial dysplasia - A novel mouse model providing insights into geleophysic dysplasia

Keyphrases

• ADAMTSL2 100%
• At Birth 10%
• Binding Protein 20%
• Brachydactyly 10%
• Bronchial Epithelial Cells 100%
• Bronchial Epithelium 20%
• Bronchial Smooth muscle Cells 10%
• Bronchial Stenosis 10%
• Bronchial Wall 10%
• Cardiac Valves 10%
• Dysregulation 20%
• Embryonic Lung Development 10%
• Epithelial Dysplasia 100%
• Extracellular Matrix 10%
• FBN2 30%
• Fibrillin Microfibrils 100%
• Fibrillin-1 (FBN1) 40%
• Geleophysic Dysplasia 100%
• Glycogen 10%
• Growth Factor Binding 10%
• Growth Factor Signaling 10%
• Joint Contracture 10%
• LacZ Reporter 10%
• Lethal Conditions 10%
• Marfan Syndrome 10%
• Microfibril-associated Glycoprotein 10%
• Microfibrils 40%
• Mouse Model 100%
• Neutralizing Antibodies 10%
• Non-lethal 10%
• Short Stature 20%
• Skin Fibrosis 10%
• Stiff Skin 10%
• Surface Glycoprotein 10%
• Transforming Growth Factor-β 50%

Medicine and Dentistry

• Brachydactyly 16%
• Bronchial Epithelium 33%
• Bronchus Stenosis 16%
• Childbirth 16%
• Disease 16%
• Epithelial Dysplasia 100%
• Extracellular Matrix 16%
• Fibrillin 100%
• Fibrillin 1 66%
• Geleophysic Dysplasia 100%
• Glycoprotein 33%
• Heart Valve 16%
• Joint Contracture 16%
• Lung Development 16%
• Marfan Syndrome 16%
• Neutralization 16%
• Neutralizing Antibody 16%
• Pregnancy 16%
• Protein Binding 33%
• Short Stature 33%
• Skin Fibrosis 16%
• Smooth Muscle Cell 16%
• Synapsin I 33%
• Transforming Growth Factor 83%

Biochemistry, Genetics and Molecular Biology

• Binding Protein 20%
• Body Height 20%
• Dysplasia 100%
• Fibrillin 100%
• Glycoprotein 20%
• Lung Development 10%
• Marfan's Syndrome 10%
• Mouse 50%
• Mouse Model 100%
• Neutralizing Antibody 10%
• Pregnancy 10%
• Synapsin I 20%
• Transforming Growth Factor 50%